New Avenues of Research in Fatty Acid Oxidation and Ketone Body Metabolism: the scientific legacy of Derek Williamson

Contents

IN MEMORIAM
1 Analysis of free and conjugated varanic acid diastereomers using HPLC electrospray tandem mass spectrometry in patients with D-bifunctional protein deficiency Vreken P, Overmars H, van Lint L, Hunneman D.H., Wanders R.J.A.	Pages 1-4
2 Comparative effects of hemipalmitoylcarnitinium stereoisomers on hepatic mitochondrial carnitine palmitoyltransferases in the diabetic rat Nicole E. Neptune, Prashant S. Savle, Isabella U. Nam, Richard D. Gandour, and Khosrow Kashfi	Pages 5-9
3 Fatty acid regulation of gene expression in adipogenesis and adipocyte metabolism Eric Duplus, Martine Glorian and Claude Forest	Pages 11-16
4 Co-regulation of mitochondrial glycerol-3-phosphate acyltransferase and carnitine palmitoyltransferase I mRNA expression in carnitine- depleted rat liver and heart P. Degrace, L. Demizieux, J. Gresti and P. Clouet	Pages 17-21
5 Shifted cooperation of desaturation and oxidation of palmitic acid in rat liver L. Demizieux, P. Degrace, J. Gresti, M. Narce, J.-P. Poisson and P. Clouet	Pages 23-27
6 Co-ordination of oxidative and non-oxidative metabolism: a pivotal role for the pyruvate dehydrogenase kinases Mary C. Sugden and Mark J. Holness	Pages 29-32
7 Mitochondrial carnitine/acylcarnitine translocase deficiency L. IJlst, J.P.N. Ruiter, C.W.T. van Roermund and R.J.A. Wanders	Pages 33-37
8 D-3-Hydroxybutyrate dehydrogenase, a ketone body converting enzyme: regulation during the hibernation process M. Kabine, M. Cherkaoui Malki, N. Latruffe and M.S. El Kebbaj	Pages 39-43
9 Fatty acid oxidation in Saccharomyces cerevisiae and the functional role of peroxisomal and cytosolic malate dehydrogenase in the re-oxidation of intraperoxisomal NADH C.W.T. van Roermund and R.J.A. Wanders	Pages 45-50
10 2-Methyl branched-chain fatty acid ƒÀ-oxidation in peroxisomes and mitochondria and the role of 2-methylacyl-CoA racemase therein S. Ferdinandusse, S. Denis, P. Vreken, H.R. Waterham and R.J.A. Wanders	Pages 51-57
11 2-Methyl-3-hydroxybutyryl-CoA dehydrogenase deficiency, a new disorder of isoleucine and branched-chain fatty acid degradation: studies on the forward and reverse reactions R.J.A. Wanders, J.P.N. Ruiter, S. Kuiper, J. Brand, M. Lindner, G. F. Hoffman, E. Mayatapek and J. Zschocke	Pages 59-61
12 Peroxisomes and PPARs : a key role in metabolism and cell differentiation Joseph Vamecq, Louis Vallee and Norbert Latruffe	Pages 63-69

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